Restrictive lung disease refers to a group of thoracic deformities that result in inefficient coupling between the respiratory muscles and the thoracic cage. The disorders are usually characterised by a restrictive defect and share the potential to cause long term hypercapnic respiratory failure.1
The most common thoracic abnormality leading to respiratory failure is thoracoplasty. Scoliosis and/or kyphoscoliosis may also cause severe respiratory failure. Symptoms of respiratory failure include:
dyspnoea on exertion1
poor sleep quality1
loss of appetite.
Shneerson JM, Simonds AK. Non-invasive ventilation for chest wall and neuromuscular disorders. Eur Respir J. 2002; 20:480-487